Hematologic Malignancy
Nasal Type Extranodal NK/T-Cell Lymphoma
CI-CAN-00006107Explore in graph →
Hematologic25 active trials
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Hematologic Malignancy
CI-CAN-00006107Explore in graph →
Data completeness2 / 7 dimensions
Computed from entity_counters.completeness · refreshed after each connector run
Definition
An aggressive, predominantly extranodal, mature T-cell non-Hodgkin lymphoma. It is characterized by an often angiocentric and angiodestructive cellular infiltrate composed of EBV positive NK/T cells. The nasal cavity is the most common site of involvement. Patients often present with midfacial destructive lesions (lethal midline granuloma). The disease may disseminate rapidly to various anatomic sites including the gastrointestinal tract, skin, testis, and cervical lymph nodes. It is also known as angiocentric T-cell lymphoma. The term "polymorphic reticulosis" has been widely used to describe the morphologic changes seen in this type of lymphoma. However, the latter term may also apply to lymphomatoid granulomatosis, which is an angiocentric and angiodestructive EBV positive B-cell lymphoproliferative disorder.
Data updated 22 days agoSource updated 26.08e
Taxonomy
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Parents
Children (7)
Anatomy
8 descendants in total; counters on this page aggregate over all of them.
Data updated 5 hours agoSource updated unknowncounters aggregate over descendants
Names
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Key figures
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Data updated 5 hours agoSource updated unknownregistry figures: cdc-uscs · latest year available per metric · counters aggregate over descendants