Skip to content

CancerIndexthe global index of cancer

Cancers Data Trials Drugs Genes Biomarkers Approvals Rankings Research gap Graph

Cancers Data Trials Drugs Genes Biomarkers Approvals Rankings Research gap Graph

Pulse Data updates Year in cancer Taxonomy Countries Compare Trial intelligence Trial map Drug pipeline Sources Methodology About Trust & policies Data downloads Developers (API)

Loading cancer entity…

CancerIndex

CancerIndex is a research and information platform. It is not a physician, does not diagnose, and does not recommend treatment. Population statistics do not predict individual outcomes.

Every number links to its source and retrieval date. Derived metrics carry a formula version. AI-generated synthesis is not enabled in this phase; all content is database-grounded.

About Trust & policies Data explorer Data downloads Pulse Data update log Developers (API)Sources Methodology Taxonomy Countries Compare Contact · contact@spboucher.ai Status

© 2026 CancerIndex · built and maintained by Simon-Pierre Boucher · contact contact@spboucher.ai · hosted on MacLustr (www.maclustr.io). Source data remains under the license of each provider — see /sources.

Sezary Syndrome · CancerIndex

Cancers
Neoplasm
Neoplasm by Morphology
Hematopoietic and Lymphoid Cell Neoplasm
Lymphocytic Neoplasm
Lymphoid Leukemia
Leukemic Phase of Non-Hodgkin Lymphoma
Sezary Syndrome

Hematologic Malignancy

Sezary Syndrome

CI-CAN-00006676Explore in graph →

Hematologic11 active trials1 evidence items

NCIt: C3366
OncoTree: SS
DOID: 8541
UMLS CUI: C0036920
MeSH: D012751

Overview
Statistics
Survival
Genomics
Variants & evidence1
Drugs1
Trials56
Research
Rankings
Sources & provenance

Data completeness3 / 7 dimensions

Epidemiology (no data yet)
Survival (no data yet)
Trials (data present)
Literature (data present)
Genomics (no data yet)
Evidence (data present)
Therapies (no data yet)

Computed from entity_counters.completeness · refreshed after each connector run

Definition

What this entity is

A generalized peripheral (mature) T-cell neoplasm characterized by the presence of erythroderma, lymphadenopathy, and neoplastic, cerebriform T-lymphocytes in the blood. Sezary syndrome is an aggressive disease. (WHO, 2001)

Definition text as published by ncit-evsProvenance

Source: NCI Thesaurus (NCIt)
Dataset: NCI Thesaurus
Version: 26.08e
Retrieved: Sep 8, 2026
Layer: raw (as published)
Evidence: expert curation
License: CC BY 4.0
Run: ING-NCITEVS-20260908-000001

Open at source Curated

Data updated 22 days agoSource updated 26.08e

Taxonomy

Position in the hierarchies

Several hierarchies coexist; edges are listed per hierarchy type with their source.

Parents

ncit

Leukemic Phase of Non-Hodgkin LymphomaHematologic Malignancy
Mycosis Fungoides and Sezary SyndromeHematologic Malignancy

oncotree

T-Cell Non-Hodgkin LymphomaHematologic Malignancy

Children (0)

Leaf node — no children.

Anatomy

Anatomical sites

Hematopoietic and Lymphatic SystemC35813

Record

Identity

CancerIndex ID: CI-CAN-00006676
Entity type: Hematologic Malignancy
Malignant: Yes
Solid / hematologic: Hematologic
Pediatric relevant: Not flagged
Rare cancer: Unknown (no incidence data yet)
Hierarchy depth: 6
Classification version: 26.08e
Semantic types: Neoplastic Process
Status: Active
Record updated: 2026-09-08

Coverage

Data completeness

Trials (all / active)

56 / 11

Publications (all / 5y)

2,140 / 342

Evidence items

1

Genes / variants

1 / 1

Drugs (any / approved)

1 / 0

Genomic cohorts

0

Epidemiology / survival obs.

0 / 0

Data updated 18 hours agoSource updated unknowncounters aggregate over descendants

Names

Synonyms (10)

Sezary Syndromemesh_heading · MeSH
CTCL / Sezary syndromesynonym · NCIt
Cutaneous T-cell lymphoma/Sezary syndromesynonym · NCIt
Erythroderma, Sezarysynonym · MeSH
Lymphoma, Sezary'ssynonym · MeSH
Sezary diseasesynonym · NCIt
Sezary disease, unspecified sitesynonym · NCIt
Sezary Lymphomasynonym · MeSH
Sezary's Diseasesynonym · NCIt
Sezary Syndromesynonym · OncoTree

CancerIndex is a research and information platform. It does not diagnose and does not recommend treatment.

Key figures

At a glance

Each figure carries its unit, period and source; ranks link to "Why this rank?".

US deaths19,882countUnited States · 2024 · both sexes · all agescdc-wonderObservedrank #8 of 31 (USA · both sexes · all ages · 2024 · top-level cancers)figures shown for Non-Hodgkin Lymphoma (registry level) — open Non-Hodgkin Lymphoma
US new cases75,946countUnited States · 2023 · both sexes · all agescdc-uscsObservedrank #8 of 32 (USA · both sexes · all ages · 2023 · top-level cancers)figures shown for Non-Hodgkin Lymphoma (registry level) — open Non-Hodgkin Lymphoma
US age-standardized mortality4.5per 100,000United States · 2024 · both sexes · all ages · 2000 U.S. Std. Populationcdc-wonderObservedrank #7 of 23 (USA · both sexes · all ages · 2024 · top-level cancers)figures shown for Non-Hodgkin Lymphoma (registry level) — open Non-Hodgkin Lymphoma
Active trials11countcurrent registry status · entity + descendantsclinicaltrialsComputedrank #572 of 1,654 (World · both sexes · all ages · latest · all malignant entities)
Recruiting trials5countstatus RECRUITING · entity + descendantsclinicaltrialsComputedrank #583 of 1,277 (World · both sexes · all ages · latest · all malignant entities)
Curated evidence items1countaccepted CIViC items · entity + descendantscivicComputedrank #392 of 492 (World · both sexes · all ages · latest · all malignant entities)
Publications, last 12 months45countPubMed records · stored query · 12-month windowpubmedComputedrank #476 of 2,294 (World · both sexes · all ages · latest · all malignant entities)
Genomic cohorts0countopen GDC projects · entity + descendantsgdcComputednot in a current ranking snapshot

Data updated 18 hours agoSource updated unknownregistry figures: cdc-uscs · latest year available per metric · counters aggregate over descendants