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Pleomorphic Rhabdomyosarcoma · CancerIndex

Cancers
Neoplasm
Neoplasm by Special Category
Malignant Neoplasm
Sarcoma
Myosarcoma
Rhabdomyosarcoma
Pleomorphic Rhabdomyosarcoma

Subtype

Pleomorphic Rhabdomyosarcoma

CI-CAN-00006454Explore in graph →

5 active trials

NCIt: C4258
OncoTree: PLRMS
DOID: 3250
UMLS CUI: C0334480

Overview
Statistics
Survival
Genomics
Variants & evidence
Drugs
Trials11
Research
Rankings
Sources & provenance

Data completeness2 / 7 dimensions

Epidemiology (no data yet)
Survival (no data yet)
Trials (data present)
Literature (data present)
Genomics (no data yet)
Evidence (no data yet)
Therapies (no data yet)

Computed from entity_counters.completeness · refreshed after each connector run

Definition

What this entity is

An aggressive malignant mesenchymal neoplasm with skeletal muscle differentiation, occurring in adults and rarely in children. The tumor is characterized by the presence of bizarre round, spindle, and polygonal cells. Clinical presentation includes a rapidly enlarging painful mass usually of the lower extremities.

Definition text as published by ncit-evsProvenance

Source: NCI Thesaurus (NCIt)
Dataset: NCI Thesaurus
Version: 26.08e
Retrieved: Sep 8, 2026
Layer: raw (as published)
Evidence: expert curation
License: CC BY 4.0
Run: ING-NCITEVS-20260908-000001

Open at source Curated

Data updated 22 days agoSource updated 26.08e

Taxonomy

Position in the hierarchies

Several hierarchies coexist; edges are listed per hierarchy type with their source.

Parents

ncit

RhabdomyosarcomaSubtype

oncotree

RhabdomyosarcomaSubtype

Children (2)

ncit

Adult Pleomorphic Rhabdomyosarcoma
Childhood Pleomorphic Rhabdomyosarcoma

Anatomy

Anatomical sites

Connective and Soft TissueC3810

Record

Identity

CancerIndex ID: CI-CAN-00006454
Entity type: Subtype
Malignant: Yes
Solid / hematologic: Solid tumor
Pediatric relevant: Not flagged
Rare cancer: Unknown (no incidence data yet)
Hierarchy depth: 6
Classification version: 26.08e
Semantic types: Neoplastic Process
Status: Active
Record updated: 2026-09-08

Coverage

Data completeness

Trials (all / active): 11 / 5

Publications (all / 5y)

298 / 79

Evidence items

0

Genes / variants

0 / 0

Drugs (any / approved)

0 / 0

Genomic cohorts

0

Epidemiology / survival obs.

0 / 0

Data updated 11 hours agoSource updated unknowncounters aggregate over descendants

Names

Synonyms (1)

Pleomorphic Rhabdomyosarcomasynonym · OncoTree

CancerIndex is a research and information platform. It does not diagnose and does not recommend treatment.

Key figures

At a glance

Each figure carries its unit, period and source; ranks link to "Why this rank?".

No registry-level ancestor: burden figures are published for the mutually exclusive top-level site groups only, and this entity does not descend from one. Global figures (IARC / GLOBOCAN) stay under license review and SEER awaits credentials.

Active trials5countcurrent registry status · entity + descendantsclinicaltrialsComputedrank #752 of 1,654 (World · both sexes · all ages · latest · all malignant entities)
Recruiting trials3countstatus RECRUITING · entity + descendantsclinicaltrialsComputedrank #677 of 1,284 (World · both sexes · all ages · latest · all malignant entities)
Curated evidence items0countaccepted CIViC items · entity + descendantscivicComputednot in a current ranking snapshot
Publications, last 12 months20countPubMed records · stored query · 12-month windowpubmedComputedrank #723 of 2,294 (World · both sexes · all ages · latest · all malignant entities)
Genomic cohorts0countopen GDC projects · entity + descendantsgdcComputednot in a current ranking snapshot

Data updated 11 hours agoSource updated unknownregistry figures: none · counters aggregate over descendants