- NCIt
- C5576
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Data completeness1 / 7 dimensions
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Definition
A rare undifferentiated sarcoma with overlapping features of atypical fibroxanthoma. It occurs in severely sun-damaged skin of elderly patients and usually affects the head and neck region. It manifests with rapidly growing nodules and plaques. Morphologically, it is characterized by dermal proliferation of pleomorphic spindle cells. Epithelioid and multinucleated giant cells may by present. The tumor grows in a fascicular or storiform pattern and invades subcutaneous adipose tissue, skeletal muscle, and fascia. Tumor cell necrosis, perineural invasion, and lymphatic invasion may also be seen. There is increased mitotic activity with atypical mitoses present. Local recurrences occur in 20-30% of cases and metastases in 10-20% of cases.
Data updated 22 days agoSource updated 26.08e
Taxonomy
Several hierarchies coexist; edges are listed per hierarchy type with their source.
Parents
Children (0)
Leaf node — no children.
Anatomy
Data updated 55 minutes agoSource updated unknowncounters aggregate over descendants
Names
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Key figures
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No registry-level ancestor: burden figures are published for the mutually exclusive top-level site groups only, and this entity does not descend from one. Global figures (IARC / GLOBOCAN) stay under license review and SEER awaits credentials.
Data updated 55 minutes agoSource updated unknownregistry figures: none · counters aggregate over descendants