Subtype

PEComa

CI-CAN-00003639Explore in graph →

Non-malignant10 active trials3 evidence items

NCIt: C38150
OncoTree: PECOMA
DOID: 2643
UMLS CUI: C1300127
MeSH: D054973

Data completeness2 / 7 dimensions

Epidemiology (no data yet)
Survival (no data yet)
Trials (data present)
Literature (no data yet)
Genomics (no data yet)
Evidence (data present)
Therapies (no data yet)

Computed from entity_counters.completeness · refreshed after each connector run

Definition

What this entity is

A soft tissue mesenchymal neoplasm with perivascular epithelioid cell differentiation. Representative examples include angiomyolipoma, clear cell-sugar-tumor of the lung, and lymphangioleiomyomatosis.

Definition text as published by ncit-evs Curated

Data updated 22 days agoSource updated 26.08e

Taxonomy

Position in the hierarchies

Several hierarchies coexist; edges are listed per hierarchy type with their source.

Parents

ncit

Soft Tissue Neoplasm of Uncertain DifferentiationSubtype

Children (13)

ncit

Angiomyolipoma3 sub
Benign PEComa3 sub
Bladder PEComa2 sub
Childhood PEComa1 sub
Clear Cell Myomelanocytic Tumor of the Falciform Ligament/Ligamentum Teres
Digestive System PEComa3 sub
Lung PEComa3 sub
Lymphangioleiomyoma
Lymphangioleiomyomatosis

Anatomy

Anatomical sites

2 sub

Malignant PEComa3 sub

Sclerosing PEComa

Skin PEComa1 sub

Uterine Corpus PEComa2 sub

35 descendants in total; counters on this page aggregate over all of them.

Publications (all / 5y)

0 / 0

Evidence items

3

Genes / variants

1 / 1

Drugs (any / approved)

0 / 0

Genomic cohorts

0

Epidemiology / survival obs.

0 / 0

Data updated 34 minutes agoSource updated unknowncounters aggregate over descendants

Names

Synonyms (5)

Perivascular Epithelioid Cell Neoplasmsmesh_heading · MeSH
Neoplasm with Perivascular Epithelioid Cell Differentiationsynonym · NCIt
PEComassynonym · MeSH
Perivascular Epithelioid Cell Tumorsynonym · OncoTree
Tumor with Perivascular Epithelioid Cell Differentiationsynonym · NCIt

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Key figures

At a glance

Each figure carries its unit, period and source; ranks link to "Why this rank?".

No registry-level ancestor: burden figures are published for the mutually exclusive top-level site groups only, and this entity does not descend from one. Global figures (IARC / GLOBOCAN) stay under license review and SEER awaits credentials.

Active trials10countcurrent registry status · entity + descendantsclinicaltrialsComputednot in a current ranking snapshot
Recruiting trials5countstatus RECRUITING · entity + descendantsclinicaltrialsComputednot in a current ranking snapshot
Curated evidence items3countaccepted CIViC items · entity + descendantscivicComputednot in a current ranking snapshot
Publications, last 12 months0countPubMed records · stored query · 12-month windowpubmedComputednot in a current ranking snapshot
Genomic cohorts0countopen GDC projects · entity + descendantsgdcComputednot in a current ranking snapshot

Data updated 34 minutes agoSource updated unknownregistry figures: none · counters aggregate over descendants