Subtype
Polymorphous Low Grade Neuroepithelial Tumor of the Young
CI-CAN-00003713PLNTYExplore in graph →
Non-malignant1 evidence items
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Subtype
CI-CAN-00003713PLNTYExplore in graph →
Data completeness1 / 7 dimensions
Computed from entity_counters.completeness · refreshed after each connector run
Definition
A low-grade cerebral tumor associated with seizures and in many cases refractory epilepsy. It usually occurs in the second and third decades of life. It is characterized by the presence of oligodendroglioma-like components. It may also contain astrocytic components. MAPK pathway-activating genetic alterations play a role in the development of this tumor. Causative gene alterations include mutations resulting in the expression of BRAF p.V600E and gene fusions involving FGFR2 or FGFR3 genes. IDH gene mutations and 1p/19q codeletion are not present.
Data updated 22 days agoSource updated 26.08e
Taxonomy
Several hierarchies coexist; edges are listed per hierarchy type with their source.
Children (0)
Leaf node — no children.
Anatomy
Data updated 18 hours agoSource updated unknowncounters aggregate over descendants
Names
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Key figures
Each figure carries its unit, period and source; ranks link to "Why this rank?".
No registry-level ancestor: burden figures are published for the mutually exclusive top-level site groups only, and this entity does not descend from one. Global figures (IARC / GLOBOCAN) stay under license review and SEER awaits credentials.
Data updated 18 hours agoSource updated unknownregistry figures: none · counters aggregate over descendants