Cancer Family
Malignant Peritoneal and Retroperitoneal Neoplasm
CI-CAN-00000248Explore in graph →
- NCIt
- C156711
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Cancer Family
CI-CAN-00000248Explore in graph →
Genomics
4 cohorts mapped to this entity or its descendants. Each frequency is affected / profiled within one cohort; cohorts are shown separately because case selection, sequencing depth and definitions differ. By default the cohort with the most cases profiled is shown.
92 cases with simple somatic mutation data · 92 cases total · Data Release 46.0 · mapped to Adrenal Cortical Carcinoma ALIAS
| # | Gene | Alteration | Affected (n) | Profiled (n) | Frequency (%) | Source |
|---|---|---|---|---|---|---|
| 1 | LRP1 | Ssm | 71 | 92 | 77.2% | gdc |
| 2 | HSD17B6 | Ssm | 70 | 92 | 76.1% | gdc |
| 3 | BAZ2A | Ssm | 70 | 92 | 76.1% | gdc |
| 4 | NACA | Ssm | 70 | 92 | 76.1% | gdc |
| 5 | CAND1 | Ssm | 70 | 92 | 76.1% | gdc |
| 6 | AVPR1A | Ssm | 70 | 92 | 76.1% | gdc |
| 7 | TSPAN31 | Ssm | 69 | 92 | 75% | gdc |
| 8 | AGAP2 | Ssm | 69 |
Data updated 22 days agoSource updated Data Release 46.0
90 cases with simple somatic mutation data · 92 cases total · 2026-01-05 · mapped to Adrenal Cortical Carcinoma EXACT_IDENTIFIER
| # | Gene | Alteration | Affected (n) | Profiled (n) | Frequency (%) | Source |
|---|---|---|---|---|---|---|
| 1 | ZFPM1 | Ssm | 47 |
90 cases with simple somatic mutation data · 92 cases total · 2026-02-04 · mapped to Adrenal Cortical Carcinoma EXACT_IDENTIFIER
| # | Gene | Alteration | Affected (n) | Profiled (n) | Frequency (%) | Source |
|---|---|---|---|---|---|---|
| 1 | TP53 | Ssm | 15 |
91 cases with simple somatic mutation data · 92 cases total · 2026-06-05 · mapped to Adrenal Cortical Carcinoma EXACT_IDENTIFIER
| # | Gene | Alteration | Affected (n) | Profiled (n) | Frequency (%) | Source |
|---|---|---|---|---|---|---|
| 1 |
Cohorts mapped to a descendant (e.g. a subtype) are included because their cases belong to this entity by definition; the mapping and its match type are shown per cohort.
| 92 |
| 75% |
| gdc |
| 9 | CDK4 | Ssm | 69 | 92 | 75% | gdc |
| 10 | MARCHF9 | Ssm | 69 | 92 | 75% | gdc |
| 11 | AC117378.1 | Ssm | 69 | 92 | 75% | gdc |
| 12 | PTGES3 | Ssm | 69 | 92 | 75% | gdc |
| 13 | CYP27B1 | Ssm | 69 | 92 | 75% | gdc |
| 14 | BIN2 | Ssm | 69 | 92 | 75% | gdc |
| 15 | KMT2D | Ssm | 69 | 92 | 75% | gdc |
| 16 | TSFM | Ssm | 69 | 92 | 75% | gdc |
| 17 | OS9 | Ssm | 69 | 92 | 75% | gdc |
| 18 | CTDSP2 | Ssm | 69 | 92 | 75% | gdc |
| 19 | FRS2 | Ssm | 69 | 92 | 75% | gdc |
| 20 | EEF1AKMT3 | Ssm | 69 | 92 | 75% | gdc |
| 21 | ATP23 | Ssm | 69 | 92 | 75% | gdc |
| 22 | ATP5F1B | Ssm | 69 | 92 | 75% | gdc |
| 23 | PRIM1 | Ssm | 69 | 92 | 75% | gdc |
| 24 | AVIL | Ssm | 69 | 92 | 75% | gdc |
| 25 | RBMS2 | Ssm | 69 | 92 | 75% | gdc |
| 26 | IL22 | Ssm | 69 | 92 | 75% | gdc |
| 27 | METTL1 | Ssm | 69 | 92 | 75% | gdc |
| 28 | ZBTB39 | Ssm | 69 | 92 | 75% | gdc |
| 29 | DYRK2 | Ssm | 69 | 92 | 75% | gdc |
| 30 | STAT6 | Ssm | 69 | 92 | 75% | gdc |
| 90 |
| 52.2% |
| cbioportal |
| 2 | MUC5B | Ssm | 35 | 90 | 38.9% | cbioportal |
| 3 | GARS1 | Ssm | 34 | 90 | 37.8% | cbioportal |
| 4 | ZNF517 | Ssm | 33 | 90 | 36.7% | cbioportal |
| 5 | LRIG1 | Ssm | 31 | 90 | 34.4% | cbioportal |
| 6 | MUC2 | Ssm | 28 | 90 | 31.1% | cbioportal |
| 7 | LACTB | Ssm | 27 | 90 | 30% | cbioportal |
| 8 | OBSCN | Ssm | 27 | 90 | 30% | cbioportal |
| 9 | CCDC102A | Ssm | 26 | 90 | 28.9% | cbioportal |
| 10 | OPRD1 | Ssm | 26 | 90 | 28.9% | cbioportal |
| 11 | SOWAHA | Ssm | 26 | 90 | 28.9% | cbioportal |
| 12 | TOR3A | Ssm | 25 | 90 | 27.8% | cbioportal |
| 13 | USP42 | Ssm | 25 | 90 | 27.8% | cbioportal |
| 14 | CRIPAK | Ssm | 24 | 90 | 26.7% | cbioportal |
| 15 | PODXL | Ssm | 24 | 90 | 26.7% | cbioportal |
| 16 | ZNF787 | Ssm | 24 | 90 | 26.7% | cbioportal |
| 17 | TRIOBP | Ssm | 23 | 90 | 25.6% | cbioportal |
| 18 | MAL2 | Ssm | 22 | 90 | 24.4% | cbioportal |
| 19 | MUC16 | Ssm | 22 | 90 | 24.4% | cbioportal |
| 20 | IRX3 | Ssm | 21 | 90 | 23.3% | cbioportal |
| 21 | MUC4 | Ssm | 21 | 90 | 23.3% | cbioportal |
| 22 | TPO | Ssm | 21 | 90 | 23.3% | cbioportal |
| 23 | TMEM247 | Ssm | 20 | 90 | 22.2% | cbioportal |
| 24 | ASPDH | Ssm | 19 | 90 | 21.1% | cbioportal |
| 25 | ERCC2 | Ssm | 19 | 90 | 21.1% | cbioportal |
| 26 | GLTPD2 | Ssm | 19 | 90 | 21.1% | cbioportal |
| 27 | KCNK17 | Ssm | 19 | 90 | 21.1% | cbioportal |
| 28 | OTOP1 | Ssm | 19 | 90 | 21.1% | cbioportal |
| 29 | RINL | Ssm | 19 | 90 | 21.1% | cbioportal |
| 30 | SALL3 | Ssm | 19 | 90 | 21.1% | cbioportal |
Data updated 22 days agoSource updated 2026-01-05
| 90 |
| 16.7% |
| cbioportal |
| 2 | MUC16 | Ssm | 14 | 90 | 15.6% | cbioportal |
| 3 | CTNNB1 | Ssm | 13 | 90 | 14.4% | cbioportal |
| 4 | TTN | Ssm | 10 | 90 | 11.1% | cbioportal |
| 5 | ASXL3 | Ssm | 7 | 90 | 7.8% | cbioportal |
| 6 | CNTNAP5 | Ssm | 7 | 90 | 7.8% | cbioportal |
| 7 | PCDH15 | Ssm | 7 | 90 | 7.8% | cbioportal |
| 8 | PKHD1 | Ssm | 7 | 90 | 7.8% | cbioportal |
| 9 | DST | Ssm | 6 | 90 | 6.7% | cbioportal |
| 10 | HMCN1 | Ssm | 6 | 90 | 6.7% | cbioportal |
| 11 | LRP1 | Ssm | 6 | 90 | 6.7% | cbioportal |
| 12 | NF1 | Ssm | 6 | 90 | 6.7% | cbioportal |
| 13 | SVEP1 | Ssm | 6 | 90 | 6.7% | cbioportal |
| 14 | APOB | Ssm | 5 | 90 | 5.6% | cbioportal |
| 15 | ATM | Ssm | 5 | 90 | 5.6% | cbioportal |
| 16 | CMYA5 | Ssm | 5 | 90 | 5.6% | cbioportal |
| 17 | CSMD1 | Ssm | 5 | 90 | 5.6% | cbioportal |
| 18 | FAT4 | Ssm | 5 | 90 | 5.6% | cbioportal |
| 19 | FBN2 | Ssm | 5 | 90 | 5.6% | cbioportal |
| 20 | FRAS1 | Ssm | 5 | 90 | 5.6% | cbioportal |
| 21 | KMT2B | Ssm | 5 | 90 | 5.6% | cbioportal |
| 22 | MEN1 | Ssm | 5 | 90 | 5.6% | cbioportal |
| 23 | PRKAR1A | Ssm | 5 | 90 | 5.6% | cbioportal |
| 24 | TENM2 | Ssm | 5 | 90 | 5.6% | cbioportal |
| 25 | TUT7 | Ssm | 5 | 90 | 5.6% | cbioportal |
| 26 | ADGRG4 | Ssm | 4 | 90 | 4.4% | cbioportal |
| 27 | AHNAK2 | Ssm | 4 | 90 | 4.4% | cbioportal |
| 28 | ANK2 | Ssm | 4 | 90 | 4.4% | cbioportal |
| 29 | ANK3 | Ssm | 4 | 90 | 4.4% | cbioportal |
| 30 | COL4A6 | Ssm | 4 | 90 | 4.4% | cbioportal |
Data updated 22 days agoSource updated 2026-02-04
| TP53 |
| Ssm |
| 18 |
| 91 |
| 19.8% |
| cbioportal |
| 2 | CTNNB1 | Ssm | 14 | 91 | 15.4% | cbioportal |
| 3 | MUC16 | Ssm | 14 | 91 | 15.4% | cbioportal |
| 4 | TTN | Ssm | 10 | 91 | 11% | cbioportal |
| 5 | HMCN1 | Ssm | 8 | 91 | 8.8% | cbioportal |
| 6 | PCDH15 | Ssm | 8 | 91 | 8.8% | cbioportal |
| 7 | PKHD1 | Ssm | 8 | 91 | 8.8% | cbioportal |
| 8 | ASXL3 | Ssm | 7 | 91 | 7.7% | cbioportal |
| 9 | CNTNAP5 | Ssm | 7 | 91 | 7.7% | cbioportal |
| 10 | DST | Ssm | 7 | 91 | 7.7% | cbioportal |
| 11 | FAT4 | Ssm | 7 | 91 | 7.7% | cbioportal |
| 12 | MEN1 | Ssm | 7 | 91 | 7.7% | cbioportal |
| 13 | HRNR | Ssm | 6 | 91 | 6.6% | cbioportal |
| 14 | KMT2B | Ssm | 6 | 91 | 6.6% | cbioportal |
| 15 | MUC4 | Ssm | 6 | 91 | 6.6% | cbioportal |
| 16 | OBSCN | Ssm | 6 | 91 | 6.6% | cbioportal |
| 17 | SVEP1 | Ssm | 6 | 91 | 6.6% | cbioportal |
| 18 | ADGRV1 | Ssm | 5 | 91 | 5.5% | cbioportal |
| 19 | AHNAK2 | Ssm | 5 | 91 | 5.5% | cbioportal |
| 20 | ANK2 | Ssm | 5 | 91 | 5.5% | cbioportal |
| 21 | APOB | Ssm | 5 | 91 | 5.5% | cbioportal |
| 22 | ATM | Ssm | 5 | 91 | 5.5% | cbioportal |
| 23 | CMYA5 | Ssm | 5 | 91 | 5.5% | cbioportal |
| 24 | CSMD1 | Ssm | 5 | 91 | 5.5% | cbioportal |
| 25 | DNAH10 | Ssm | 5 | 91 | 5.5% | cbioportal |
| 26 | DNAH5 | Ssm | 5 | 91 | 5.5% | cbioportal |
| 27 | EYS | Ssm | 5 | 91 | 5.5% | cbioportal |
| 28 | FBN2 | Ssm | 5 | 91 | 5.5% | cbioportal |
| 29 | FLG | Ssm | 5 | 91 | 5.5% | cbioportal |
| 30 | FRAS1 | Ssm | 5 | 91 | 5.5% | cbioportal |
Data updated 22 days agoSource updated 2026-06-05