- NCIt
- C5751
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Data completeness0 / 7 dimensions
Computed from entity_counters.completeness · refreshed after each connector run
Definition
A multicystic mesenchymal tumor that arises from the liver during fetal development and is characterized by the presence of hypocellular fibromyxoid stroma and bland spindle cell proliferation. Cytogenetic and molecular studies have revealed the presence of chromosomal rearrangements involving chromosome 19q13.4 or androgenetic-biparental mosaicism. These findings support the evidence that it is a neoplastic process and not only a developmental process. Clinically, it usually presents as an abdominal mass associated with abdominal distention. It generally has a benign clinical course. Following resection, the prognosis is good.
Data updated 22 days agoSource updated 26.08e
Taxonomy
Several hierarchies coexist; edges are listed per hierarchy type with their source.
Parents
Children (0)
Leaf node — no children.
Anatomy
Data updated 5 hours agoSource updated unknowncounters aggregate over descendants
Names
CancerIndex is a research and information platform. It does not diagnose and does not recommend treatment.
Key figures
Each figure carries its unit, period and source; ranks link to "Why this rank?".
No registry-level ancestor: burden figures are published for the mutually exclusive top-level site groups only, and this entity does not descend from one. Global figures (IARC / GLOBOCAN) stay under license review and SEER awaits credentials.
Data updated 5 hours agoSource updated unknownregistry figures: none · counters aggregate over descendants