Molecular Subtype

Intracranial Mesenchymal Tumor, FET-CREB Fusion-Positive

CI-CAN-00002937Explore in graph →

Non-malignant

NCIt: C186614

Data completeness0 / 7 dimensions

Epidemiology (no data yet)
Survival (no data yet)
Trials (no data yet)
Literature (no data yet)
Genomics (no data yet)
Evidence (no data yet)
Therapies (no data yet)

Computed from entity_counters.completeness · refreshed after each connector run

Definition

What this entity is

A provisional entity that refers to a group of neoplasms with a broad morphological spectrum, characterized by fusion of a FET family gene (usually EWSR1 and rarely FUS) with a member of the CREB family of transcription factors (CREB1, ATF1, or CREM). It includes entities previously termed intracranial angiomatoid fibrous histiocytoma or intracranial myxoid mesenchymal tumor. It is usually located in the supratentorial brain and mostly affects children and young adults. There is a spectrum of clinical behaviors ranging from slowly growing tumors to rapid recurrences, and rarely metastases.

Definition text as published by ncit-evs Curated

Data updated 22 days agoSource updated 26.08e

Taxonomy

Position in the hierarchies

Several hierarchies coexist; edges are listed per hierarchy type with their source.

Parents

ncit

Central Nervous System Mesenchymal, Non-Meningothelial NeoplasmSubtype
Primary Brain NeoplasmSubtype

Children (0)

Leaf node — no children.

Anatomy

Anatomical sites

Publications (all / 5y)

0 / 0

Evidence items

0

Genes / variants

0 / 0

Drugs (any / approved)

0 / 0

Genomic cohorts

0

Epidemiology / survival obs.

0 / 0

Data updated 28 minutes agoSource updated unknowncounters aggregate over descendants

Names

Synonyms (2)

Intracranial Mesenchymal Tumor /Angiomatoid Fibrous Histiocytomasynonym · NCIt
Intracranial Mesenchymal Tumor with FET-CREB Fusionsynonym · NCIt

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Key figures

At a glance

Each figure carries its unit, period and source; ranks link to "Why this rank?".

No registry-level ancestor: burden figures are published for the mutually exclusive top-level site groups only, and this entity does not descend from one. Global figures (IARC / GLOBOCAN) stay under license review and SEER awaits credentials.

Active trials0countcurrent registry status · entity + descendantsclinicaltrialsComputednot in a current ranking snapshot
Recruiting trials0countstatus RECRUITING · entity + descendantsclinicaltrialsComputednot in a current ranking snapshot
Curated evidence items0countaccepted CIViC items · entity + descendantscivicComputednot in a current ranking snapshot
Publications, last 12 months0countPubMed records · stored query · 12-month windowpubmedComputednot in a current ranking snapshot
Genomic cohorts0countopen GDC projects · entity + descendantsgdcComputednot in a current ranking snapshot

Data updated 28 minutes agoSource updated unknownregistry figures: none · counters aggregate over descendants