Hematologic Malignancy
Erdheim-Chester Disease
CI-CAN-00000850ECDExplore in graph →
HematologicNon-malignant6 active trials
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Hematologic Malignancy
CI-CAN-00000850ECDExplore in graph →
Data completeness1 / 7 dimensions
Computed from entity_counters.completeness · refreshed after each connector run
Definition
A very rare, multisystem non-Langerhans cell histiocytosis that predominantly affects adults. It is characterized by the proliferation in the tissues of lipid-laden macrophages and the presence of multinucleated giant cells. It results in sclerosis of the long bones and failure of the affected organs. Patients may present with bone pain, exophthalmos, ataxia, liver failure, kidney failure, and hypopituitarism.
Data updated 22 days agoSource updated 26.08e
Taxonomy
Several hierarchies coexist; edges are listed per hierarchy type with their source.
Parents
Anatomy
Data updated 19 hours agoSource updated unknowncounters aggregate over descendants
Names
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Key figures
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No registry-level ancestor: burden figures are published for the mutually exclusive top-level site groups only, and this entity does not descend from one. Global figures (IARC / GLOBOCAN) stay under license review and SEER awaits credentials.
Data updated 19 hours agoSource updated unknownregistry figures: none · counters aggregate over descendants