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Endolymphatic Sac Tumor · CancerIndex

Cancers
Neoplasm
Neoplasm by Morphology
Epithelial Neoplasm
Papillary Epithelial Neoplasm
Papillary Carcinoma
Papillary Adenocarcinoma
Endolymphatic Sac Tumor

Subtype

Endolymphatic Sac Tumor

CI-CAN-00005157ELSTExplore in graph →

1 active trials

NCIt: C67560

Overview
Statistics
Survival
Genomics
Variants & evidence
Drugs
Trials1
Research
Rankings
Sources & provenance

Data completeness2 / 7 dimensions

Epidemiology (no data yet)
Survival (no data yet)
Trials (data present)
Literature (data present)
Genomics (no data yet)
Evidence (no data yet)
Therapies (no data yet)

Computed from entity_counters.completeness · refreshed after each connector run

Definition

What this entity is

A rare, low-grade malignant epithelial tumor arising from the endolymphatic sac in the temporal bone. Morphologically, it is characterized by the presence of papillary and cystic structures. As tumors grow, they may destroy petrous temporal bone and extend into the middle ear and the middle and posterior cranial fossae and into the cerebellopontine angle. (WHO 2017)

Definition text as published by ncit-evsProvenance

Source: NCI Thesaurus (NCIt)
Dataset: NCI Thesaurus
Version: 26.08e
Retrieved: Sep 8, 2026
Layer: raw (as published)
Evidence: expert curation
License: CC BY 4.0
Run: ING-NCITEVS-20260908-000001

Open at source Curated

Data updated 22 days agoSource updated 26.08e

Taxonomy

Position in the hierarchies

Several hierarchies coexist; edges are listed per hierarchy type with their source.

Parents

ncit

Malignant Inner Ear NeoplasmSubtype
Papillary AdenocarcinomaHistology

Children (0)

Leaf node — no children.

Anatomy

Anatomical sites

Head and NeckC12418

Record

Identity

CancerIndex ID: CI-CAN-00005157
Entity type: Subtype
Malignant: Yes
Solid / hematologic: Solid tumor
Pediatric relevant: Not flagged
Rare cancer: Unknown (no incidence data yet)
Hierarchy depth: 6
Classification version: 26.08e
Semantic types: Neoplastic Process
Status: Active
Record updated: 2026-09-08

Coverage

Data completeness

Trials (all / active): 1 / 1

Publications (all / 5y)

293 / 91

Evidence items

0

Genes / variants

0 / 0

Drugs (any / approved)

0 / 0

Genomic cohorts

0

Epidemiology / survival obs.

0 / 0

Data updated 4 hours agoSource updated unknowncounters aggregate over descendants

Names

Synonyms (2)

Heffner Tumorsynonym · NCIt
Low Grade Papillary Adenocarcinoma of Endolymphatic Sac Originsynonym · NCIt

CancerIndex is a research and information platform. It does not diagnose and does not recommend treatment.

Key figures

At a glance

Each figure carries its unit, period and source; ranks link to "Why this rank?".

No registry-level ancestor: burden figures are published for the mutually exclusive top-level site groups only, and this entity does not descend from one. Global figures (IARC / GLOBOCAN) stay under license review and SEER awaits credentials.

Active trials1countcurrent registry status · entity + descendantsclinicaltrialsComputedrank #1186 of 1,654 (World · both sexes · all ages · latest · all malignant entities)
Recruiting trials1countstatus RECRUITING · entity + descendantsclinicaltrialsComputedrank #893 of 1,284 (World · both sexes · all ages · latest · all malignant entities)
Curated evidence items0countaccepted CIViC items · entity + descendantscivicComputednot in a current ranking snapshot
Publications, last 12 months18countPubMed records · stored query · 12-month windowpubmedComputedrank #762 of 2,294 (World · both sexes · all ages · latest · all malignant entities)
Genomic cohorts0countopen GDC projects · entity + descendantsgdcComputednot in a current ranking snapshot

Data updated 4 hours agoSource updated unknownregistry figures: none · counters aggregate over descendants